{"id":3461,"date":"2014-07-26T15:31:25","date_gmt":"2014-07-26T15:31:25","guid":{"rendered":"https:\/\/higuey.info\/news\/news\/?p=3461"},"modified":"2020-11-21T16:51:34","modified_gmt":"2020-11-21T16:51:34","slug":"muere-uno-de-los-bebes-gemelos-con-sindrome-de-arlequin","status":"publish","type":"post","link":"https:\/\/higuey.info\/news\/muere-uno-de-los-bebes-gemelos-con-sindrome-de-arlequin\/","title":{"rendered":"Muere uno de los beb\u00e9s gemelos con s\u00edndrome de Arlequ\u00edn."},"content":{"rendered":"<p><a href=\"https:\/\/higuey.info\/news\/wp-content\/uploads\/2014\/07\/hospital.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-large wp-image-3462\" src=\"https:\/\/higuey.info\/news\/wp-content\/uploads\/2014\/07\/hospital-550x365.jpg\" alt=\"Recorrido por Hospital Robert Reid Cabral\" width=\"550\" height=\"365\" srcset=\"https:\/\/higuey.info\/news\/wp-content\/uploads\/2014\/07\/hospital-550x365.jpg 550w, https:\/\/higuey.info\/news\/wp-content\/uploads\/2014\/07\/hospital-300x199.jpg 300w, https:\/\/higuey.info\/news\/wp-content\/uploads\/2014\/07\/hospital-220x146.jpg 220w, https:\/\/higuey.info\/news\/wp-content\/uploads\/2014\/07\/hospital.jpg 645w\" sizes=\"auto, (max-width: 550px) 100vw, 550px\" \/><\/a>[&#8212;]<\/p>\n<p>SANTO DOMINGO, Rep\u00fablica Dominicana.-La directora del\u00a0 Hospital Infantil Dr. Robert Reid Cabral, Rosa Nieves Paulino, inform\u00f3 que en la tarde de este viernes, 25 de julio, falleci\u00f3 uno de los gemelos que ingresaron a este centro de salud afectados con Ictiosis Arlequ\u00edn.<\/p>\n<p>[&#8212;]<\/p>\n<p>El s\u00edndrome de Arlequ\u00edn o Ictiosis Arlequ\u00edn es una enfermedad gen\u00e9tica de la piel, poco com\u00fan, que se caracteriza por escamas grandes y gruesas que aparecen en toda la piel y otras malformaciones.<\/p>\n<p>Los beb\u00e9s, de aproximadamente un mes de nacidos, ingresaron al hospital el pasado 17 del mes en curso, procedentes de <strong>Hig\u00fcey<\/strong>, ambos con\u00a0 condici\u00f3n muy\u00a0 severa y\u00a0 pron\u00f3stico reservado por las complicaciones propias de la enfermedad. Las condiciones del reci\u00e9n nacido que contin\u00faa con vida son de cuidado extremo.<\/p>\n<blockquote><p>\u201cEs la forma de\u00a0ictiosis\u00a0cong\u00e9nita m\u00e1s grave, y se hace evidente desde el nacimiento. Debe su nombre al aspecto que tienen los reci\u00e9n nacidos con la enfermedad, que recuerda a un disfraz del personaje infantil Arlequ\u00edn\u201d, indic\u00f3<\/p><\/blockquote>\n<p>\u201cLamentablemente, hoy (ayer, viernes) a las 2:40 pm,\u00a0 falleci\u00f3 de las complicaciones propias de dicha condici\u00f3n uno de los reci\u00e9n nacidos. Agradecemos a todas las personas, autoridades y de la comunidad,\u00a0 quienes\u00a0 han ofrecido su colaboraci\u00f3n y soporte ,\u00a0 a\u00a0 fines de\u00a0 mantener con\u00a0 vida a\u00a0 estos ni\u00f1os, contribuyendo con\u00a0 el personal del hospital en hacer todo lo posible en brindar calidad de vida y soporte\u201d, explic\u00f3 la doctora Nieves Paulino.<\/p>\n<p>El Hospital Dr. Roberto Reid indic\u00f3 que la Ictiosis Arlequ\u00edn\u00a0es una\u00a0enfermedad\u00a0de la piel, rara,\u00a0del grupo de las llamadas\u00a0genodermatosis\u00a0(grupo de dermatosis hereditarias con trastornos metab\u00f3licos).<\/p>\n<p>\u201cEs la forma de\u00a0ictiosis\u00a0cong\u00e9nita m\u00e1s grave, y se hace evidente desde el nacimiento. Debe su nombre al aspecto que tienen los reci\u00e9n nacidos con la enfermedad, que recuerda a un disfraz del personaje infantil Arlequ\u00edn\u201d, indic\u00f3.<\/p>\n<p>Tambi\u00e9n, quienes padecen esta enfermedad nacen con la parte interior de los p\u00e1rpados visible, por lo que en lugar de ojos se observan los p\u00e1rpados totalmente rojos. Se asocia generalmente a deformidades faciales caracter\u00edsticas y a menudo anomal\u00edas en otras partes del cuerpo, especialmente en el t\u00f3rax.<\/p>\n<blockquote>\n<p style=\"text-align: center;\"><a href=\"http:\/\/acento.com.do\/2014\/actualidad\/8159443-muere-uno-de-los-bebes-gemelos-con-sindrome-de-arlequin-informa-el-hospital-robert-reid\/?utm_source=dlvr.it&amp;utm_medium=facebook\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Visitar la Fuente<\/strong><\/a><\/p>\n<\/blockquote>\n","protected":false},"excerpt":{"rendered":"<p>Los beb\u00e9s, de aproximadamente un mes de nacidos, ingresaron al hospital el pasado 17 del mes en curso, procedentes de Hig\u00fcey, ambos con  condici\u00f3n muy  severa y  pron\u00f3stico reservado por las complicaciones propias de la enfermedad. Las condiciones del reci\u00e9n nacido que contin\u00faa con vida son de cuidado extremo.<\/p>\n","protected":false},"author":1,"featured_media":3462,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[4],"tags":[2225,2226,454,50],"class_list":["post-3461","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-higuey","tag-arlequin","tag-gemelos","tag-ninos","tag-salud-2"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Muere uno de los beb\u00e9s gemelos con s\u00edndrome de Arlequ\u00edn. - Higuey.Info<\/title>\n<meta name=\"description\" content=\"Los beb\u00e9s, de aproximadamente un mes de nacidos, ingresaron al hospital el pasado 17 del mes en curso, procedentes de Hig\u00fcey, ambos con condici\u00f3n muy severa y pron\u00f3stico reservado por las complicaciones propias de la enfermedad. 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